A case series of three patients of double-chambered right ventricle with distinctive features

Abstract

Double-chambered right ventricle (DCRV) is an extremely rare condition caused by anomalous muscular bundle (AMB), dividing the RV into high- and low-pressure chambers. We are highlighting a case series of three rare patients of DCRV, presenting with diverse clinical and echocardiographic features. Case 1 is manifesting as isolated DCRV in an asymptomatic young female adult, with the AMB located in the subvalvular region of the right ventricular outflow tract. Case 2 is of a significantly symptomatic male infant, afflicted with DCRV, and associated with a large apical muscular ventricular septal defect (VSD). The AMB was situated near the RV apex, just proximal to the VSD. Case 3 represented an asymptomatic DCRV in an adolescent female along with a coexisting small hemodynamically insignificant VSD. Individually, all the three patients are exceedingly rare and their clinical and echocardiographic features were peculiarly distinctive, hence making this case series an interesting and exemplary manuscript.