Extraskeletal mesenchymal chondrosarcoma of the abdomen: A rare clinical presentation

Authors

  • Mohammad Habib Raza
  • Mohammad Ibrahim Raza
  • Mohd Sadik Akhtar
  • Shagufta Qadri

DOI:

https://doi.org/10.32677/ijcr.v9i4.3885

Keywords:

Extraskeletal mesenchymal chondrosarcoma, Desmoid tumor, Chondroprogenitor cells, Abdominal mesenchymal chondrosarcoma

Abstract

Extraskeletal mesenchymal chondrosarcoma (EMCS) is a rare malignant soft tissue tumor of chondroprogenitor cell origin. Originally, it was restricted to the bone only but that is no longer the case. Recent literature reports that 20–33% of these tumors occur at the extraskeletal sites. We report one such case, in which the tumor involved the anterior abdominal wall muscles and also had a large intra- abdominal mass that covered a large part of the peritoneal cavity. The clinical features and computed tomography findings suggested the diagnosis of a malignant desmoid tumor with intra-abdominal extension; however, the histopathological examination and the immunohistochemistry proved the tumor to be EMCS. The case is reported due to the dilemma in diagnosis, its rarity, large size, parietal, and intra-abdominal extension with multiple site involvement.

 

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Published

2024-01-31

Issue

Section

Case Report

How to Cite

Extraskeletal mesenchymal chondrosarcoma of the abdomen: A rare clinical presentation. (2024). Indian Journal of Case Reports, 9(4), 116-118. https://doi.org/10.32677/ijcr.v9i4.3885