Case report of mucha-habermann disease

Authors

  • Archana J Lokhande
  • Rohini Soni
  • Santosh Kumar Mahto
  • Tapan Kumar Dhali

DOI:

https://doi.org/10.32677/IJCR.2018.v04.i04.022

Keywords:

Pityriasis lichenoides, Systemic corticosteroid, Ulceronecrosis

Abstract

Pityriasis lichenoides et varioliformis acuta (PLEVA), also known as a Mucha-Habermann disease, is an uncommon, idiopathic, and acquired dermatosis. The disease is characterized by erythematous, scaly, papules, and polymorphic lesions which often progresses to hemorrhagic necrosis and heals with varioliform scarring. A febrile ulceronecrotic variant of PLEVA, also termed pityriasis lichenoides (PL) with ulceronecrosis and hyperthermia (PLUH) or febrile ulceronecrotic Mucha-Habermann disease (FUMHD), is a severe variant of PLEVA. The disease is characterized by the acute onset of large, more destructive, coalescent papules, leading to ulceronecrotic skin lesions associated with high fever and other systemic symptoms. In spite of the presence of multiple treatment modalities with variable success rate, the disease has poor prognosis. Here, we report the case of a 17-year-old male patient who presented with typical features of FUMHD and responded well to systemic administration of corticosteroid therapy.

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Published

2018-08-25

Issue

Section

Case Report

How to Cite

Case report of mucha-habermann disease. (2018). Indian Journal of Case Reports, 4(4), 318-320. https://doi.org/10.32677/IJCR.2018.v04.i04.022

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