Clinico-radiological Correlation of An Uncommon presentation of Caffey’s Disease

Abstract

Caffey’s disease which is also known as infantile cortical hyperostosis usually affects young infants <6 months of age. It is a rare, mostly self-limiting disease. It is characterized by a triad of soft tissue swelling, cortical thickening of the underlying bone, and hyperirritability. The mean age of the presentation is 9-11 weeks of age. It typically involves the mandible, clavicles, ribs, and diaphysis of the long bones. We report a case of Caffey’s disease presenting at an early age of 6 weeks, affecting long bones, with symmetrical involvement of ulnar bones, and thrombocytosis as an uncommon presentation. On follow-up for 48 months, there were no recurrences.