Poland syndrome: Atypical presentation and review of literature

Abstract

Poland syndrome is a rare congenital disorder with absent or hypoplastic pectoralis major and hand anomalies. Dextroposition, female predisposition, and the left-sided anomalies in Poland syndrome are rarely reported in literature. We report a female baby who was born with chest wall defects, left hand anomalies, dextroposed heart, and hypoplastic ribs. She was diagnosed as Poland syndrome and managed conservatively.